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Clinics in Laboratory Medicine
Volume 23, Issue 1, Pages 1-256 (March 2003)

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Preface


Prion diseases free full text
Bernardino Ghetti, Pedro Piccardo
pages xv-xvi
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Color Plates
pages xvii-xlv
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Review article


Perspectives on prion biology, prion disease pathogenesis, and pharmacologic approaches to treatment
Stephen J DeArmond, Stanley B Prusiner
pages 1-41
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Hereditary Creutzfeldt-Jakob disease and fatal familial insomnia
Pierluigi Gambetti, Piero Parchi, Shu G Chen
pages 43-64
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Hereditary prion protein amyloidoses
Bernardino Ghetti, Fabrizio Tagliavini, M Takao, Orso Bugiani, Pedro Piccardo
pages 65-85
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Variant Creutzfeldt-Jakob disease
H.J.T Ward, M.W Head, R.G Will, J.W Ironside
pages 87-108
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Diagnosis of prion diseases
Hans A Kretzschmar
pages 109-128
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Transmissible spongiform encephalopathy update and implications for blood safety
Maura N Ricketts, Paul Brown
pages 129-137
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Scrapie and chronic wasting disease
Elizabeth S Williams
pages 139-159
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A gene-targeted mouse model of P102L Gerstmann-Sträussler-Scheinker syndrome
Rona M Barron, Jean C Manson
pages 161-173
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A murine model of a familial prion disease
David A Harris, Roberto Chiesa, Bettina Drisaldi, Elena Quaglio, Antonio Migheli, Pedro Piccardo, Bernardino Ghetti
pages 175-186
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Therapeutic approaches to prion diseases
Giacomina Rossi, Mario Salmona, Gianluigi Forloni, Orso Bugiani, Fabrizio Tagliavini
pages 187-208
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Three-dimensional structures of the prion protein and its doppel
Roland Riek, Thorsten Lührs
pages 209-225
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In vitro conversion of normal prion protein into pathologic isoforms
Alex Bossers, Alan Rigter, Ruth de Vries, Mari A Smits
pages 227-247
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Index
pages 249-255
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